Objective To investigate the value of transthoracic echocardiography（TTE） in the diagnosis of anomalous origin of the right pulmonary artery from the ascending aorta（AORPA）.Methods Eleven cases of AORPA diagnosed by operation or CTA were analyzed retrospectively

and the value of TTE in the diagnosis and follow-up of AORPA was discussed.Results Ten cases were diagnosed clearly while 1 case was missed by TEE before surgery

the diagnostic coincidence rate was 90.9%.The direct manifestations of TEE was the main pulmonary artery bifurcation disappeared and the abnormal right pulmonary artery originated from the ascending aorta.The indirect manifestations was moderate to severe pulmonary hypertension.In all cases

the origin of the abnormality was proximal type

which was mostly associated with other cardiac malformations（9 cases with patent ductus arteriosus

2 cases with right pulmonary artery stenosis

2 cases with ventricular septal defect

4 cases with atrial septal defect/patent foramen ovale

1 case with partial anomalous pulmonary venous connection and 1 case with aortic valve stenosis）.The surgery was performed in 10 cases with AORPA

and 1 case had not operated due to severe pulmonary hypertension.Postoperative follow-up of the 10 patients:anastomotic patency in 9 cases and right pulmonary artery stenosis in 1 case.Conclusion TTE plays an important role in the non-invasive and accurate diagnosis for clinical diagnosis and follow-up of AORPA

which indicates a good value in clinical application.