Objective：To summarize the clinical features and intervention therapeutic effects on congenital pulmonary arteriovenous fistulas（PAVFs），and to explore the method and therapeutic principle of transcatheter closure of PAVFs. Methods：The clinic manifestation，efficiency of closure and follow-up of 8 PAVFs children in Children’s Hospital of Chongqing Medical University were retrospectively analyzed from July 2004 to December 2016. Results：Transcatheter closures of all cases were successful，and there was no significance in mean pulmonary arterial pressure before and after the treatment（P=0.757）. During the follow-up period of 6 months to 10 years，no residual shunts and other complications occurred，and compared to the pre-operation，the significance was existed in oxyhemoglobin saturation and hemoglobin during the last follow-up（P<0.05）. Conclusion：Transcatheter closure treatment is a safe and effective method for congenital PAVFs in children.