Objective：To discuss the diagnosis and treatment of pulmonary artery sling（PAS）. Methods：Sixteen patients who diagnosed as PAS and received surgery in department of cardiothoracic surgery in the Children’s Hospital of Chongqing Medical University Between December 2009 and March 2013 were enrolled. Results：Sixteen patients with PAS underwent the surgery and all cases had a history of recurrent cough and wheezing. The age of patients ranged from 2 months to 3.5 years and body weight ranged from 4.5 kg to 15 kg. According to Cotton standard，14 patients in phase Ⅰ only received re-implantation of the left pulmonary artery（LPA） and 13 recovered；2 patients with trachea stenosis in phase Ⅲ received tracheoplasty at the same time but all died. Conclusion：For most PAS patients with trachea stenosis in phase Ⅰ，only re-implantation of the LPA may result in good results. For the PAS with tra－chea stenosis in phase Ⅱ and Ⅲ，early tracheoplasty for trachea stenosis remains to be discussed further.