Objective To evaluate the value of prenatal sonographic diagnosis of fetal intrahepatic portosystemic shunt. Materials and Methods The prenatal ultrasonographic features of 17 cases with intrahepatic portosystemic shunt were analyzed retrospectively. Combining with clinical data and following-up the birth progress. Results Park type: Type Ⅰ 0 case

Type Ⅱ 14 cases (82.35%)

Type Ⅲ 2 cases (11.77%)

Type Ⅳ 1 case (5.88%). 1 case had comorbidity with esophageal atresia and absent ductus venosus

1 case with bilateral kidney dysplasia and abnormal bipedal posture

2 cases with absent ductus venosus

1 case with aberrant right subclavicular artery

others were not seen comorbidity. 1 case was complicated with intrauterine growth retardation

1 case with cardiac insufficiency

the rest were not seen other complications. Pregnancy outcome: 2 cases with termination of pregnancy

1 case with intrauterine death

14 cases with natural delivery (1 case with intrauterine spontaneous closure of the shunt was included ). During follow-up period of 6-36 months postnatally

9 cases of abnormal shunt closed spontaneously

2 cases underwent interventional embolization

1 case was still persistent with the shunt and 1 case was lost to follow-up. Conclusion Prenatal ultrasonography has high diagnostic accuracy for fetal intrahepatic portosystemic shunt and provides important reference information for clinical intervention after birth.