苗勒管发育不全综合征合并先天性肛门直肠畸形的临床研究新焦点

王佚; 孙静

doi:10.16016/j.1000-5404.201804157

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苗勒管发育不全综合征合并先天性肛门直肠畸形的临床研究新焦点

专题报道：儿童先天性直肠肛门畸形的诊治 | 更新时间：2026-01-09

- 苗勒管发育不全综合征合并先天性肛门直肠畸形的临床研究新焦点
- New focuses in diagnosis and treatment of Mayer-Rokitanski-Küster-Hauser syndrome with congenital anorectal malformation
- 第三军医大学学报 2018年40卷第23期页码：2126-2130
- 作者机构：
  
  400014 重庆, 重庆医科大学附属儿童医院胃肠新生儿外科
- 作者简介：
  
  [ 王佚, 博士, 主任医师, 教授, 硕士研究生导师。重庆医科大学附属儿童医院外科教研室副主任, 胃肠新生儿外科主任。担任中华医学会小儿外科分会肿瘤学组副组长, 中国医师协会新生儿分会委员, 重庆市医院协会外科管理专业委员会常务委员, 重庆市小儿外科专委会委员, 《中华小儿外科杂志》编委等。承担国家自然科学基金, 重庆市自然科学基金, 重庆市教委及重庆市卫计委重点项目等6项。在SCI及国内核心期刊上发表论文40余篇。主要从事儿童消化道畸形临床及基础方面的研究。E-mail: wy757311@hotmail.com WANG Yi, E-mail:wy757311@hotmail.com
- 基金信息：
- DOI：10.16016/j.1000-5404.201804157
  中图分类号： R726.571;R726.911
- 收稿：2018-04-23，
  
  修回：2018-09-30，
  
  纸质出版：2018-12-15
- 稿件说明：
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王佚, 孙静. 苗勒管发育不全综合征合并先天性肛门直肠畸形的临床研究新焦点[J]. 第三军医大学学报, 2018,40(23):2126-2130.

Yi WANG, Jing SUN. New focuses in diagnosis and treatment of Mayer-Rokitanski-Küster-Hauser syndrome with congenital anorectal malformation[J]. Journal of Third Military Medical University, 2018, 40(23): 2126-2130.
王佚, 孙静. 苗勒管发育不全综合征合并先天性肛门直肠畸形的临床研究新焦点[J]. 第三军医大学学报, 2018,40(23):2126-2130. DOI： 10.16016/j.1000-5404.201804157.

Yi WANG, Jing SUN. New focuses in diagnosis and treatment of Mayer-Rokitanski-Küster-Hauser syndrome with congenital anorectal malformation[J]. Journal of Third Military Medical University, 2018, 40(23): 2126-2130. DOI： 10.16016/j.1000-5404.201804157.

摘要

Abstract

Mayer-Rokitanski-Küster-Hauser (MRKH) syndrome with congenital anorectal malformations (ARM) is a rare disease in children

which involves the female anorectal and reproductive system. Treatment and prognosis for this condition are still inconclusive. Although the understanding for congenital ARM has been deepened in recent years

attentions having been paid to MRKH syndrome with ARM are far from enough. Its treatment and timing are controversial. Rectal vestibular fistula is the most common type of female imperforate anus. When the exact vaginal opening has not been identified by perineal examination

the complication of MRKH syndrome should be considered. This article systematically reviewed the clinical diagnosis

treatment

timing and prognosis of MRKH syndrome with imperforate anus.

关键词

Keywords

references

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