
浏览全部资源
扫码关注微信
纸质出版:2011
移动端阅览
解芳,朱岷,曹艳丽,熊丰.特发性矮小SHOX基因异常X线骨骼特征[J].陆军军医大学学报(原第三军医大学学报),2011,33(06):604-607.
Xie Fang,Zhu Min,Cao Yanli,Xiong Feng.Correlation of SHOX gene deficiency and mutation with skeleton X-ray characteristics of idiopathic short stature patients[J].J Amry Med Univ (J Third Mil Med Univ),2011,33(06):604-607.
解芳,朱岷,曹艳丽,熊丰.特发性矮小SHOX基因异常X线骨骼特征[J].陆军军医大学学报(原第三军医大学学报),2011,33(06):604-607. DOI:
Xie Fang,Zhu Min,Cao Yanli,Xiong Feng.Correlation of SHOX gene deficiency and mutation with skeleton X-ray characteristics of idiopathic short stature patients[J].J Amry Med Univ (J Third Mil Med Univ),2011,33(06):604-607. DOI:
目的 研究特发性矮小(idiopathic short stature,ISS)中矮小同源盒基因(short stature homeobox-containing gene,SHOX)缺失和突变与X线骨骼特征指标的关系。 方法 采用微卫星分析及外显子测序对354例矮小症患者进行SHOX基因分析,对检测出的SHOX基因异常患者进行X线骨骼指标统计学分析。 结果 354例矮小症患者中发现SHOX基因异常35例(9.9%,35/354),其中外显子突变3例(8.6%,3/35),SHOX基因缺失32例(91.4%
32/35)。X线骨骼特征指标:SHOX基因异常组与正常组相比有轻微马德隆畸形改变,其中最突出的是SHOX异常组尺桡骨远端关节内侧面夹角明显减小(P0.05,P0.01)。 结论 SHOX基因异常者X线骨骼指标的改变有尺桡骨远端关节内侧面夹角减小、桡骨垂高增加、和尺桡骨远端高度差增加等,女性较男性改变更为明显,且有随年龄增长骨骼表现更为明显的趋势。
Objective To study the correlation of short stature homeobox-containing gene (SHOX) deficiency and mutation with skeleton X-ray characteristics of idiopathic short stature (ISS) patients. Methods Microsatellite analysis and exon sequence analysis were adopted to test SHOX deficiency and mutation in 354 ISS patients
and the results were compared with 196 controls with normal height. The ISS patients with SHOX deficiency and mutation were subjected to statistical analysis of skeleton X-ray characteristics. Results In the 354 ISS patients
abnormal SHOX were found in 35 cases (9.9%
35/354)
including 3 with exon mutation (8.6%
3/35) and 32 with SHOX deficiency (91.4%
32/35). As compared with the controls
the skeleton X-ray characteristics of the 35 ISS patients included slight Madelung deformity and obvious reduction of the included angle between the distal joint medial surfaces of the ulna and radius(P0.05
P0.01). Conclusion The skeleton X-ray characteristics of the ISS patients with abnormal SHOX gene include the reduction of the included angle between the distal joint medial surfaces of the ulna and radius
the vertical height increase of the radius
the increase of the distal height difference between the ulna and radius
etc. These characteristics are more serious in females than males and are more obvious with the increase of age.
0
浏览量
0
下载量
0
CSCD
关联资源
相关文章
相关作者
相关机构
京公网安备11010802024621