New focuses in diagnosis and treatment of Mayer-Rokitanski-Küster-Hauser syndrome with congenital anorectal malformation

Yi WANG; Jing SUN

doi:10.16016/j.1000-5404.201804157

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New focuses in diagnosis and treatment of Mayer-Rokitanski-Küster-Hauser syndrome with congenital anorectal malformation

Monographic reports:Diagnosis and treatment of anorectal malformation in children | 更新时间：2026-01-09

- New focuses in diagnosis and treatment of Mayer-Rokitanski-Küster-Hauser syndrome with congenital anorectal malformation
- Journal of Third Military Medical University Vol. 40, Issue 23, Pages: 2126-2130(2018)
- 作者机构：
  
  400014 重庆, 重庆医科大学附属儿童医院胃肠新生儿外科
- 作者简介：
- 基金信息：
- DOI：10.16016/j.1000-5404.201804157
  CLC： R726.571;R726.911
- Received：23 April 2018，
  
  Revised：2018-09-30，
  
  Published：15 December 2018
- 稿件说明：
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Yi WANG, Jing SUN. New focuses in diagnosis and treatment of Mayer-Rokitanski-Küster-Hauser syndrome with congenital anorectal malformation[J]. Journal of Third Military Medical University, 2018, 40(23): 2126-2130.
DOI：

Yi WANG, Jing SUN. New focuses in diagnosis and treatment of Mayer-Rokitanski-Küster-Hauser syndrome with congenital anorectal malformation[J]. Journal of Third Military Medical University, 2018, 40(23): 2126-2130. DOI： 10.16016/j.1000-5404.201804157.

摘要

Abstract

Mayer-Rokitanski-Küster-Hauser (MRKH) syndrome with congenital anorectal malformations (ARM) is a rare disease in children

which involves the female anorectal and reproductive system. Treatment and prognosis for this condition are still inconclusive. Although the understanding for congenital ARM has been deepened in recent years

attentions having been paid to MRKH syndrome with ARM are far from enough. Its treatment and timing are controversial. Rectal vestibular fistula is the most common type of female imperforate anus. When the exact vaginal opening has not been identified by perineal examination

the complication of MRKH syndrome should be considered. This article systematically reviewed the clinical diagnosis

treatment

timing and prognosis of MRKH syndrome with imperforate anus.

关键词

Keywords

references

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